J Korean Soc Radiol.  2012 Mar;66(3):275-277. 10.3348/jksr.2012.66.3.275.

Extra-Gastrointestinal Stromal Tumor of Retroperitoneal Origin: A Case Report

• Choi SJ
• Kim HS
• Park Y
• Choi HY

• KMID: 1439426
• DOI: http://doi.org/10.3348/jksr.2012.66.3.275

Abstract

Extragastrointestinal stromal tumors (EGIST) are relatively rare, and cases originating in the retroperitoneum even rarer. We report a 60-year-old woman who presented with an EGIST originating in the retroperitoneum. Computed tomography results demonstrated a soft tissue mass on the right side of the retroperitoneum. The tumor abutted the duodenum, head of the pancreas, and right kidney. The mass was surgically proven to be a retroperitoneal tumor and histopathologically proven to be a retroperitoneal EGIST.

MeSH Terms

Duodenum
Female
Head
Humans
Kidney
Middle Aged
Pancreas

Figure

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  Fig. 1 A 60-year-old woman with a 6.5 × 5.0 × 6.0 cm retroperitoneal mass. Post-contrast CT scans shows well circumscribed, lobulated and heterogeneous enhanced solid and cystic mass arising from retroperitoneum.

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  Fig. 2 A 60-year-old woman with a primary retroperitoneal gastrointestinal stromal tumor. A. Microscopic findings of primary retroperitoneal gastrointestinal stromal tumor. The tumor is composed of spindle shaped cells arranged in fascicular pattern (H&E staining, × 100). B. Diffuse strong positive staining for c-kit protein is observed in immunochemistry test (× 100).

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