J Korean Med Sci.  2002 Oct;17(5):718-722. 10.3346/jkms.2002.17.5.718.

Neuro-Behcet's Disease Mimicking a Cerebral Tumor: A Case Report

• Park JH
• Jung MK
• Bang CO
• Park HK
• Sung KB
• Ahn MY
• Bae WK
• Chi JG

• KMID: 1127272
• DOI: http://doi.org/10.3346/jkms.2002.17.5.718

Abstract

We report a rare case of neuro-Behcet's disease (NBD) presenting as an inflammatory pseudotumor in the brain. A 52-yr-old woman was evaluated for subacute dizziness and headache. Brain magnetic resonance (MR) imaging showed a right cerebellar mass, which disappeared 2 weeks later. After a year, recurrent mucocutaneous manifestations of Beh et's disease were observed. Immunosuppressant and steroid maintenance treatment were started. She experienced two more neurologic attacks and brain MR imaging revealed an enhancing mass in the right temporal lobe. The second attack showed a good response to steroid pulse therapy, but the third attack did not respond to steroid and her neurologic signs suggested an impending transtentorial hernia. The right temporal lobectomy was performed for the purpose of life-saving. The pathologic finding of the mass was a chronic inflammatory vasculitis, compatible with NBD.

Keyword

Pseudotumor; Inflammatory Vasculitis; Steroid; Magnetic Resonance Imaging; Hernia; Cerebral

MeSH Terms

Behcet Syndrome/*diagnosis/surgery
Brain Diseases/*diagnosis/surgery
Brain Neoplasms/*diagnosis
Diagnosis, Differential
Female
Granuloma, Plasma Cell/*diagnosis/surgery
Humans
Magnetic Resonance Imaging
Middle Aged