- Anesthetic management of living donor liver transplantation for complement factor H deficiency hemolytic uremic syndrome: a case report
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Park SH, Kim GS
- KMID: 2237956
- Korean J Anesthesiol.
- 2014 Jun;66(6):481-485.
- doi: 10.4097/kjae.2014.66.6.481
We experienced a living donor liver transplantation for a 26-month-old girl with complement factor H deficiency. Complement factor H is a plasma protein that regulates the activity of the complement... -
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- Atypical HUS caused by anti-complement factor H antibody: a hematologist's perspective
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Kumar M, Mandal P, De R, Mukherjee , Dolai TK, Bhattyacharyya M
- KMID: 1787918
- Blood Res.
- 2015 Mar;50(1):63-65.
- doi: 10.5045/br.2015.50.1.63
No abstract available. -
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- Complement regulation: physiology and disease relevance
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Cho H
- KMID: 2140664
- Korean J Pediatr.
- 2015 Jul;58(7):239-244.
- doi: 10.3345/kjp.2015.58.7.239
The complement system is part of the innate immune response and as such defends against invading pathogens, removes immune complexes and damaged self-cells, aids organ regeneration, confers neuroprotection, and engages... -
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- Depositions of Complement Components and Their Inhibitors in Atuto - immune Dermatoses
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Lee CW, Kim JH, Whang KW
- KMID: 2038919
- Korean J Dermatol.
- 1990 Apr;28(2):179-186.
The complement system is known to be involved in the pathogenesis of the skin lesions in pernphigus vulgaris, bullous pemphigoid, dermatitis herpetiformis, epidermolysis bullosa acquisita, and systemic lupus erythematosus. Authors... -
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- Atypical Hemolytic Uremic Syndrome in a 13-year-old Lao Girl: A Case Report
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Kedsatha P, Cheong HI, Choi Y
- KMID: 2448161
- Child Kidney Dis.
- 2019 Apr;23(1):43-47.
- doi: 10.3339/jkspn.2019.23.1.43
Atypical hemolytic uremic syndrome (aHUS), a rare form of thrombotic microangiopathy, is distinguished from the typical form by the absence of a preceding verotoxin-producing Escherichia coli infection. Notably, aHUS occurs... -
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- A Case of Familial Atypical Hemolytic Uremic Syndrome Associated with Complement Factor H Mutation in Adults
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Lee HK, Na HK, Lee JY, Chang JW, Yang WS, Kim SB, Park JS, Park SK, Kwon SK, Cheong HI
- KMID: 1465949
- Korean J Nephrol.
- 2009 May;28(3):259-264.
The hemolytic uremic syndrome is a clinical syndrome defined by the presence of thrombocytopenia, microangiopathic hemolytic anemia and acute renal failure. Atypical hemolytic uremic syndrome (aHUS) which is not usually... -
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- Auxiliary Partial Orthotopic Liver Transplantations for One Pediatric Patient with Complement Factor H Deficiency and Two Adult Patients
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Suh KS, Lee HW, Cho EH, Yang SH, Cho JY, Cho YB, Yi NJ, Lee KU
- KMID: 2003591
- J Korean Soc Transplant.
- 2006 Jun;20(1):110-116.
We have performed 3 cases of APOLT in one child and two adults. The child recipient had suffered from complement factor H deficiency since 3 months after birth and at... -
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- Expression of Complement Regulator Genes in Abeta1-42 Stimulated Human Neuroblastoma Cell
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Choi YS, Lee KS, Kim SH
- KMID: 2343063
- J Korean Neurol Assoc.
- 2003 Oct;21(5):513-520.
BACKGROUND: Endogenous complement inhibitors in the brain may protect against the neuroinflammation in Alzheimer's disease. Human neuroblastoma cells were stimulated by Abeta1 - 4 2 to investigate whether the expression... -
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- Kidney Transplantation in Patients with Atypical Hemolytic Uremic Syndrome due to Complement Factor H Deficiency: Impact of Liver Transplantation
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Kim S, Park E, Min SI, Yi NJ, Ha J, Ha IS, Cheong HI, Kang HG
- KMID: 2399161
- J Korean Med Sci.
- 2018 Jan;33(1):e4.
- doi: 10.3346/jkms.2018.33.e4
BACKGROUND: Atypical hemolytic uremic syndrome (aHUS) is a rare disease that is often associated with genetic defects. Mutations of complement factor H (CFH) are the most common genetic defects that... -
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- Hemolytic uremic syndrome
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Park HW
- KMID: 2279304
- Korean J Pediatr.
- 2007 Oct;50(10):931-937.
- doi: 10.3345/kjp.2007.50.10.931
The hemolytic uremic syndrome (HUS) is a rare disease of microangiopathic hemolytic anemia, low platelet count and renal impairment. HUS usually occurs in young children after hemorrhagic colitis by shigatoxin-producing... -
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- Reactive Oxygen Species Production, Expression of Complement Regulator Genes and Phagocytosis in the Murine Microglial Cell after Administration of Beta-Amyloid(A beta1-42) Protein
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Choi YS, Lee KS, Kim SH
- KMID: 1626985
- J Korean Neurol Assoc.
- 2005 Feb;23(1):88-95.
BACKGROUND: Microglia is a primary cellular component of neuritic plaques in Alzheimer's disease. Beta amyloid deposits attract microglia and activate them to produce inflammatory mediators. The objectives of this study... -
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- Clinical Practice Guidelines for the Management of Atypical Hemolytic Uremic Syndrome in Korea
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Cheong HI, Jo SK, Yoon SS, Cho H, Kim JS, Kim YO, Koo JR, Park Y, Park YS, Shin JI, Yoo KH, Oh D
- KMID: 2468240
- J Korean Med Sci.
- 2016 Oct;31(10):1516-1528.
- doi: 10.3346/jkms.2016.31.10.1516
Atypical hemolytic uremic syndrome (aHUS) is a rare syndrome characterized by micro-angiopathic hemolytic anemia, thrombocytopenia, and acute kidney injury. The major pathogenesis of aHUS involves dysregulation of the complement system.... -
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