- Family of Li-Fraumeni Syndrome with a Germline Mutation in the p53 Gene
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Shin HJ, Kwon YJ, Lim YJ, Park BK, Ghim TT, Shin SH, Kong SY, Hong EK, Park HJ
- KMID: 2168956
- Clin Pediatr Hematol Oncol.
- 2009 Apr;16(1):38-42.
Li-Fraumeni syndrome is an autosomal dominant familial cancer syndrome characterized by a diverse set of tumors, including sarcoma, breast cancer, brain tumor, adrenocortical carcinoma, and acute leukemia, affecting family members.... -
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- Role of Cyclosporine A in Pediatric Patients with Refractory Chronic Idiopathic Thrombocytopenic Purpura
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Kim MJ, Kim HS, Kwon SY, Won SC, Kim BS, Choi SY, Lyu CJ
- KMID: 2168951
- Clin Pediatr Hematol Oncol.
- 2009 Apr;16(1):1-8.
PURPOSE: Since the treatment of chronic idiopathic thrombocytopenic purpura (ITP) remains unsatisfactory in patients refractory to standard therapy, alternative therapies such as splenectomy, danazol, rituximab and cyclosporine A (CsA) are... -
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- A Case of Cystic Partially Differentiated Nephroblastoma
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Baek DW, Kim HS, Kwon SY, Kim BS, Choi SY, Cho NH, Won SC, Lyu CJ
- KMID: 2168954
- Clin Pediatr Hematol Oncol.
- 2009 Apr;16(1):27-31.
Cystic partially differentiated nephroblastoma is a rare renal mass in children. Since its clinical characteristics and radiologic findings are very similar to those of cystic Wilms tumor and cystic... -
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- Effective Management of Kaposiform Hemangioendotheliomas Associatedwith Kasabach-Merritt Syndrome Using Chemotherapy
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Kim MJ, Jin JH, Lee JE, Cheong WS, Choi GS, Kim JM, Kim SK
- KMID: 2168959
- Clin Pediatr Hematol Oncol.
- 2009 Apr;16(1):54-58.
Although Kaposiform hemangioendothelioma (KHE) is a rare benign tumor, it is well known for its aggressiveness, showing mortality rates as high as 24% when progressed to Kasabach- Meritt syndrome.... -
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- A Case of Autologous Cord Blood Stem Cell Transplantationin Stage IV Neuroblastoma
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Chae JH, Kim HS, Kwon SY, Won SC, Kim BS, Choi SY, Lyu CJ
- KMID: 2168953
- Clin Pediatr Hematol Oncol.
- 2009 Apr;16(1):21-26.
Since High dose chemotherapy (HDCT) with autologous hematopoietic stem cell (HSC) rescue has been reported to be the most effective current treatment modality in advanced and refractory neuroblastoma, various types... -
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- A Case of Hemophagocytic Syndrome Induced by Adenovirus Infection after Splenectomy
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Park SH, Lee KS
- KMID: 2168958
- Clin Pediatr Hematol Oncol.
- 2009 Apr;16(1):49-53.
Hemophagocytic lymphohistiocytosis (HLH) is a rare but sometimes fatal disease. Its main features are prolonged fever, hepatosplenomegaly, cytopenias, and hemophagocytosis in the bone marrow, lymph nodes and other tissues. Hemophagocytic... -
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- Langerhans Cell Histiocytosis in a Two-month-old Infant
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Baek JM, Sohn SY, Yang JH, Woo CW, Kim YS, Kim IH, Lee J, Lee K
- KMID: 2168955
- Clin Pediatr Hematol Oncol.
- 2009 Apr;16(1):32-37.
Langerhans cell histiocytosis (LCH) is a rare condition characterized by the proliferation of distinctive histiocytes. The clinical manifestations and outcomes of LCH vary from a skin-only self-healing condition to... -
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- Thiamine Deficiency Manifested by Wernicke's Encephalopathy and Wet Beriberi in a Patient with Rhabdomyosarcoma Following Chemotherapy and Total Parenteral Nutrition
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Joo JW, Baek HJ, Han DK, Yang EM, Chung TW, Kook H, Hwang TJ
- KMID: 2168957
- Clin Pediatr Hematol Oncol.
- 2009 Apr;16(1):43-48.
Beriberi and Wernicke's encephalopathy (WE) are potentially lethal, serious diseases caused by thiamine deficiency. The most common cause is malnutrition associated with chronic alcoholism, but it may occur in... -
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- Clinical Characteristics and Treatment Outcome of Infantile Acute Lymphoblastic Leukemia
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Cho HJ, Han DK, Baek HJ, Park EY, Lee SJ, Kook H, Hwang TJ
- KMID: 2168952
- Clin Pediatr Hematol Oncol.
- 2009 Apr;16(1):9-20.
PURPOSE: Acute lymphoblastic leukemia (ALL) in infancy accounts for about 2~4% cases of childhood ALL and is biologically different from that of older children with an extremely poor prognosis. The... -
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