Korean J Gastroenterol.  2009 Oct;54(4):201-204. 10.4166/kjg.2009.54.4.201.

A Case of Caroli Disease with Biliary Stones

• Cha BH
• Lee SH
• Hwang JH
• Kim SY
• Kim H

• KMID: 783224
• DOI: http://doi.org/10.4166/kjg.2009.54.4.201

Abstract

No abstract available.

MeSH Terms

Adult
Bile Ducts, Intrahepatic/pathology
Caroli Disease/complications/*diagnosis/pathology
Gallstones/complications/*diagnosis/radiography
Humans
Male
Tomography, X-Ray Computed

Figure

• 

  Fig. 1. Pancreatico-bliliary CT and MRCP findings. (A) Non-contrast image. In segment IV/VIII of left lobe of liver, multiple high attenuated stones were found (arrowhead). (B) Contrast-enhanced image. This image showed focal low attenuated cystic dilatation of right intrahepatic duct (arrowhead). It also showed no definite dilatation of intrahepatic duct in other segments of the liver.

• 

  Fig. 2. MRCP findings. (A) T2-weighted image. MRCP image showed a cystic dilatation of IHD containing multiple stones, adjacent to the right hepatic duct (arrowhead). (B) T2-weighted image. There were multiple filling defects which reflected stones in distal common bile duct (arrowhead).

• 

  Fig. 3. ERCP finding showed cystic dilatation of IHD in right hepatic duct with multiple filling defects due to stones (arrowhead). This cystic lesion had communication with common hepatic duct, significant features to diagnose as Caroli's diseas. It also had some defects suggesting distal common bile duct stones (arrow). In this procedure, brown pigmented stone was removed with retrieval basket successfully.

• 

  Fig. 4. Pathological findings. (A) Gross examination of the specimen demonstrated cystic dilatation of the bile duct. (B-D) The bile duct wall showed fibrous thickening, chronic inflammation, and denudation of the surface epithelial lining. A small focus of remaining epithelium was noted (D, arrowheads) (B-D: Hematoxylin-Eosin; original magnification ×10 (B), ×40 (C) and ×100 (D)).

Reference

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