Korean J Intern Med.
2000 Jan;15(1):89-92.
Systemic mononuclear inflammatory vasculopathy associated with Sjogren's syndrome in a patient with primary biliary cirrhosis
- Affiliations
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- 1Department of Internal Medicine, Catholic University Medical College, Holy Family Hospital, Kyunggi-Do, Korea.
- 2Division of Rheumatology, Department of Radiology, Kangnam St. Mary's Hospital, College of Medicine, Catholic University of Korea, Seoul, Korea.
- 3Department of Clinical Pathology, Kangnam St. Mary's Hospital, College of Medicine, Catholic University of Korea, Seoul, Korea.
Abstract
- We report a 46-year-old woman with primary biliary cirrhosis (PBC) presenting with Sjogren's syndrome and systemic mononuclear inflammatory vasculopathy. Biopsy specimens of sural nerve showed findings consistent with vasculitic neuropathy. Perivascular inflammatory mononuclear cell infiltration was observed on muscle biopsy specimen. The findings of abdominal computed tomography and brain magnetic resonance imaging were suggestive of vasculitis. Clinical manifestations and radiologic findings were improved after high dose prednisolone therapy.
Keyword
MeSH Terms
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Biopsy, Needle
Case Report
Diagnosis, Differential
Female
Follow-Up Studies
Human
Liver Cirrhosis, Biliary/diagnosis+ACo-
Liver Cirrhosis, Biliary/complications+ACo-
Middle Age
Prednisone/administration +ACY- dosage
Sjogren's Syndrome/pathology
Sjogren's Syndrome/diagnosis+ACo-
Sjogren's Syndrome/complications
Sural Nerve/pathology
Treatment Outcome
Vasculitis/pathology
Vasculitis/drug therapy
Vasculitis/diagnosis+ACo-
Vasculitis/complications
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