Korean J Med.
2004 Jan;66(1):80-85.
A case of primary biliary cirrhosis manifestated with idiopathic thrombocytopenic purpura and Sjogren's syndrome
- Affiliations
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- 1Department of Internal Medicine, School of Medicine, Kyung Hee University, Seoul, Korea. kimbh@khmc.or.kr
- 2Department of Pathology, School of Medicine, Kyung Hee University, Seoul, Korea.
Abstract
- Primary biliary cirrhosis (PBC) is rare in Korea. Although its pathogenesis is not fully understood, immunologic dysregulation is suspected because it is frequently associated with other immunologic disorders. A few cases of primary biliary cirrhosis associated with idiopathic thrombocytopenic purpura (ITP) has previously been reported. However, PBC associated with ITP and Sjogren's syndrome simultaenously has not been reported yet. We experienced a 72-year-old woman had been finally diagnosed as PBC, ITP and Sjogren's syndrome. To the best of our knowledge, this is the first case in the world. We report this case with review of related literature.
