J Audiol Otol.  2025 Jan;29(1):67-74. 10.7874/jao.2024.00311.

A Case of Bilateral Sudden Deafness Caused by Wernicke Encephalopathy

• Hong Y
• Kim H
• Lee DH

• KMID: 2564440
• DOI: http://doi.org/10.7874/jao.2024.00311

Abstract

Wernicke encephalopathy, also known as thiamine deficiency, is characterized by a triad of symptoms: ophthalmoplegia, ataxia, and confusion. However, additional symptoms may manifest depending on the area affected by the lesion. Although multiple cranial neuropathies are possible, sudden onset bilateral hearing loss has been described in rare situations as the first manifestation of Wernicke encephalopathy. Here, we present a case report detailing the clinical experience of a patient diagnosed with Wernicke encephalopathy, whose initial presentation included sudden bilateral deafness. The patient was a 57-year-old man with alcoholism who was successfully diagnosed with Wernicke encephalopathy, and his hearing improved after high-dose intravenous thiamine therapy. Our case study results and a literature review indicate that video findings and suppression head impulse tests can be used to evaluate Wernicke encephalopathy.

Keyword

Sudden deafness; Central hearing loss; Thiamine; Wernicke encephalopathy