J Cerebrovasc Endovasc Neurosurg.  2024 Dec;26(4):412-417. 10.7461/jcen.2024.E2024.05.002.

Multiple AVM with separate nidi, a case report and review the literatures

• Taheri M
• Rahmatian A
• Javadnia P

• KMID: 2563091
• DOI: http://doi.org/10.7461/jcen.2024.E2024.05.002

Abstract

Multiple arteriovenous malformations (AVMs) are uncommon, accounting for only 0.3–3.2% of all AVM cases. These AVMs are often found in syndromic pediatrics of HHT and WMS. Consideration of the patient’s condition, the angioarchitecture of each AVM, and the hemodynamic connection of AVMs is crucial in determining the optimal therapeutic approach. However, the optimal therapeutic decision-making for these complex vascular lesions can be challenging due to the scarcity of their reports and their long-term follow-up. In this report, we present the case of a young man who presented with a headache, and DSA shows three left parietal AVMs, each with a separate nidus, feeder artery, and draining vein.

Keyword

Intracranial Arteriovenous Malformations; Diagnosis; Therapeutics; Multiple AVM

Figure

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  Fig. 1. Cerebral digital subtraction angiogram (DSA) shows three separated nidi of arteriovenous malformation (AVM) supplied by different branches of left middle cerebral artery (MCA) (A to D: lateral view of the left carotid angiogram in different phases).

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