Adv Pediatr Surg.  2020 Dec;26(2):77-82. 10.13029/aps.2020.26.2.77.

Intraductal Papillary Mucinous Neoplasm of the Pancreas with Worrisome Features in a 12-Year-Old Boy

• Kang MK
• Youn JK
• Kim HY

• KMID: 2525504
• DOI: http://doi.org/10.13029/aps.2020.26.2.77

Abstract

Intraductal papillary mucinous neoplasm (IPMN) of the pancreas encompasses a wide spectrum of epithelial changes from benign adenoma to invasive adenocarcinoma. IPMN is a premalignant lesion where approximately one-third of the tumors undergo malignant transformation. This disease is prevalent in the elderly population and is rare in youth. In this case we report a 12-year-old boy with symptoms of pancreatitis with cystic lesions consistent with branch duct type-IPMN. This is the third reported case of IPMN in a pediatric patient. Our patient underwent pylorus-preserving pancreaticoduodenectomy, and through this case report we suggest when worrisome features or high-risk stigmata features are observed even in pediatric patients, surgical resection should be considered due to the potential for malignant transformation in the future.

Keyword

Pancreatic intraductal neoplasms; Pancreaticoduodenectomy