Endocrinol Metab.  2021 Dec;36(6):1312-1313. 10.3803/EnM.2021.1269.

Mucosal Neuroma Cues for Endocrine Emergency Treatment

• Choi GG
• Lee HJ
• Han HJ
• Jeong YB
• Lee HB
• Park JH

• KMID: 2523500
• DOI: http://doi.org/10.3803/EnM.2021.1269

Figure

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  Fig. 1 (A) Mucosal neuromas on the tongue are found during the initial physical examination at the time of hospital admission, although a dehydrated, cracked, and dry tongue obscures this finding. A histopathological examination was not performed for these neuromas because they were benign tumors and had no specific symptoms. (B) A photograph, taken 6 days after the ectopic adrenocorticotropic hormone syndrome was resolved by bilateral adrenalectomy, shows clearly visible lingual mucosal neuromas with thickened lips, which are typical features of multiple endocrine neoplasia type 2B (MEN2B).

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  Fig. 2 (A) Transverse neck sonographic image showing a 1.8 cm, irregular-shaped, hypoechoic nodule (white arrows) with speculated margins, heterogeneous echotexture of the solid portion, and microcalcifications located in the left lobe of the thyroid. (B) Axial contrast-enhanced computed tomography image showing heterogeneous enhancing masses in both adrenal glands (black arrows), including focal cystic components in the left adrenal mass, with diffuse dilatation of the transverse colon.

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