Yonsei Med J.  2021 May;62(5):470-473. 10.3349/ymj.2021.62.5.470.

Therapeutic Lymphatic Embolization in Pediatric Primary Intestinal Lymphangiectasia

• Kwon Y
• Kim ES
• Choe YH
• Hyun D
• Kim MJ

• KMID: 2515253
• DOI: http://doi.org/10.3349/ymj.2021.62.5.470

Abstract

Primary intestinal lymphangiectasia (IL) can cause leakage of lymphatic fluids into the gastrointestinal tract, eventually leading to protein-losing enteropathy. A 15-year-old male patient, whose disease began at the age of 8 years, recently felt worsening general weakness. After diagnosing abnormal lymphatic lesions in the duodenum through endoscopy with biopsy and contrast-enhanced magnetic resonance lymphangiography, glue embolization of the leaking duodenal lymphatic channel was successfully performed. This procedure is typically reserved for adult patients, although as shown in this case, it can be properly performed in children. His serum albumin level was initially 1.5 g/dL, but elevated to 5.0 g/dL after two sessions of lymphatic embolization. Accordingly, we suggest that embolization could potentially be considered a first-line treatment for focal lesions of primary intestinal IL.

Keyword

Primary intestinal lymphangiectasia; focal lymphangiectasis; duodenum; protein-losing enteropathy; children; lymphatic embolization