Korean J Pediatr Gastroenterol Nutr.
2004 Sep;7(2):253-259.
A Case of Primary Intestinal Lymphangiectasia
- Affiliations
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- 1Department of Pediatrics, Yonsei University College of Medicine, Seoul, Korea. KKKJHD@yumc.yonsei.ac.kr
- 2Department of Surgery, Yonsei University College of Medicine, Seoul, Korea.
- 3Department of Pathology, Yonsei University College of Medicine, Seoul, Korea.
Abstract
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Primary intestinal lymphangiectasia is a congenital lymphatic disorder in which intestinal lymphatic channels are dilated and ruptured resulting in loss of protein, lipid, and lymphocyte into the intestine or peritoneum. As a result, hypoalbuminemia, generalized edema, diarrhea are clinically manifested. We report a case of primary intestinal lymphangiectasia with generalized edema which occurred in a 7-year old boy who was treated with lipid restriction diet with medium chain triglyceride oil supplement.