Korean J Pediatr Gastroenterol Nutr.  2004 Sep;7(2):253-259.

A Case of Primary Intestinal Lymphangiectasia

Affiliations
  • 1Department of Pediatrics, Yonsei University College of Medicine, Seoul, Korea. KKKJHD@yumc.yonsei.ac.kr
  • 2Department of Surgery, Yonsei University College of Medicine, Seoul, Korea.
  • 3Department of Pathology, Yonsei University College of Medicine, Seoul, Korea.

Abstract

Primary intestinal lymphangiectasia is a congenital lymphatic disorder in which intestinal lymphatic channels are dilated and ruptured resulting in loss of protein, lipid, and lymphocyte into the intestine or peritoneum. As a result, hypoalbuminemia, generalized edema, diarrhea are clinically manifested. We report a case of primary intestinal lymphangiectasia with generalized edema which occurred in a 7-year old boy who was treated with lipid restriction diet with medium chain triglyceride oil supplement.

Keyword

Primary intestinal lymphangiectasia; Protein losing enteropathy

MeSH Terms

Child
Diarrhea
Diet
Edema
Humans
Hypoalbuminemia
Intestines
Lymphocytes
Male
Peritoneum
Protein-Losing Enteropathies
Triglycerides
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