J Korean Acad Pediatr Dent.  2019 Nov;46(4):416-421. 10.5933/JKAPD.2019.46.4.416.

Dental Management in a Patient with Congenital Insensitivity to Pain with Anhidrosis : A Case Report

  • 1Department of Pediatric Dentistry, Jeonbuk National University Dental Hospital, Korea. pedo1997@jbnu.ac.kr
  • 2Department of Pediatric Dentistry and Institute of Oral Bioscience, School of Dentistry, Jeonbuk National University, Korea.


Congenital insensitivity to pain with anhidrosis (CIPA) is a rare, autosomal recessive disorder; affected patients are characterized by inability to feel pain and to sweat over the entire body, as well as by mental retardation. Because, in the oral examination, no specific findings on soft or hard tissue may be found except possible lesions due to self-mutilation, early recognition and diagnosis are essential for these patients. Pediatric dentists must be aware of the clinical manifestations and treatment considerations related to uncontrolled body temperature, tactile hyperesthesia and lack of pain reflex. In this case report, dental management of CIPA was suggested by presenting a 6-year follow-up of young patient.


CIPA; Pain insensitivity; Anhidrosis; Self-mutilation
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