Korean J Anesthesiol.  2007 Mar;52(3):367-370. 10.4097/kjae.2007.52.3.367.

Total Intravenous Anesthetic Management of a Child with Congenital Insensitivity to Pain with Anhidrosis : A case report

• Lee SJ
• Kim YK
• Seong KW
• Kim SW

• KMID: 1937607
• DOI: http://doi.org/10.4097/kjae.2007.52.3.367

Abstract

Congenital insensitivity to pain with anhidrosis (CIPA) is a rare hereditary sensory and autonomic neuropathy. CIPA is characterized by inability to sweat, insensitivity to pain, self-mutilation, recurrent episodes of hyperpyrexia, mental retardation, and autonomic nervous system abnormality. Patients with CIPA may undergo surgery because of susceptibility to trauma, bony fracture and osteomyelitis due to insensitivity to pain. We report a child who had undergone anesthesia with total intravenous anesthesia. The anesthetic management of this condition is discussed.

Keyword

congenital insensitivity to pain with anhidrosis; propofol; remifentanil; total intravenous anesthesia

MeSH Terms

Anesthesia
Anesthesia, Intravenous
Autonomic Nervous System
Child*
Hereditary Sensory and Autonomic Neuropathies*
Humans
Intellectual Disability
Osteomyelitis
Pain Insensitivity, Congenital*
Propofol
Sweat
Propofol