J Korean Orthop Assoc.  1980 Mar;15(1):166-173. 10.4055/jkoa.1980.15.1.166.

Operative Treatment of Charcot-Marie-Tooth Disease

• Oh IS
• Lee DY

• KMID: 2450573
• DOI: http://doi.org/10.4055/jkoa.1980.15.1.166

Abstract

Since the independent reports of Charcot and Marie and of Tooth, in 1886, interest in this familial disease has centered largely in the genetic and diagnostic aspects, and yet references in the literature to Surgical management are rare and inexact. Our experience with Charcot-Marie-Tooth disease in 4 patients operated at Seoul National University Hospital during the last 3 years is reported. Of 6 cases of Charcot-Marie-Tooth disease which have been studied, 4 patients have undergone surgery for the correction or amelioration of the crippling foot deformity. The authors' operation has consisted of triple arthrodesis, medial release, lengthening of the Achilles tendon, tendon transfer which was available and present evidence that properly designed surgical treatment can correct, prevent, or materially reduce disability of the deformed feet. Of the 4 cases reported here, all have either been reviewed or the patients have been interviewed in the last year. On the basis of adequate follow-up observations, thesurgical procedure outlined have been shown to improve the crippled condition. In spite of progressive musele wasting, the operative treatment could prevent or ameliorate the deformity. Three cases of Charcot-Marie-Tooth disease were evaluated in a long-term follow-up after having undergone surgery to correct their foot deformity. Excellent results were achieved from three of them which were maintained at final follow-up, and one is being gollowed up.

MeSH Terms

Achilles Tendon
Arthrodesis
Charcot-Marie-Tooth Disease*
Congenital Abnormalities
Follow-Up Studies
Foot
Foot Deformities
Humans
Seoul
Tendon Transfer
Tooth