Korean J Ophthalmol.  2019 Jun;33(3):301-302. 10.3341/kjo.2018.0088.

Orbital Malignant Peripheral Nerve Sheath Tumor Arising from Neurofibroma

• Wy S
• Kim N

• KMID: 2448873
• DOI: http://doi.org/10.3341/kjo.2018.0088

Abstract

No abstract available.

MeSH Terms

Neurofibroma*
Orbit*
Peripheral Nerves*

Figure

• 

  Fig. 1 Radiological and histological appearance of orbital malignant peripheral nerve sheath tumor. (A) Axial and (B) coronal computed tomography scan showing extraconal mass with peripheral wall enhancement and central mottled enhancement. (C) Axial and (D) coronal view of T1-weighted contrast-enhanced with fat suppression magnetic resonance imaging demonstrating a well-defined and oval-shaped mass with low signal intensity, peripheral wall enhancement and central mottled enhancement. (E) Histopathologic finding shows small round cells in fibrillary background transitioning from low to high cellularity (hematoxylin and eosin, ×50) (F) with active cell division and atypical nuclei (hematoxylin and eosin, ×200).

Reference

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