J Korean Orthop Assoc.  1990 Dec;25(6):1624-1632. 10.4055/jkoa.1990.25.6.1624.

Intramedullary Nailing in Osteogenesis Imperfecta

• Whang KS
• Sung IH
• Kim SJ

• KMID: 2443181
• DOI: http://doi.org/10.4055/jkoa.1990.25.6.1624

Abstract

Osteogenesis imperfecta is a heterogenous group of inherited disorder, which has abnormalities in the synthesis of collagen. Among variable clinical manifestations, orthopaedic clinical features are laxity of ligament and deformities arising from frequent fractures or angulation due to skeletal fragility. We had managed 4 cases of osteogensis imperfecta, which were belonged to type IV-B in two cases, type I-A in one, and type I-B in remained one by Sillence classification and they had suffered from recent fractures or deformities due to previous fractures in the long bones of the lower extremities. These patients had been treated with various types of intramedullary nails, such as Bailey-Dubow extensile rod. Rush rod and Kuntcher nail, and the result of intramedullary nailing lead to improvement of walking ability.

Keyword

Osteogenesis imperfecta; Intramedullary nailing

MeSH Terms

Classification
Collagen
Congenital Abnormalities
Fracture Fixation, Intramedullary*
Humans
Ligaments
Lower Extremity
Osteogenesis Imperfecta*
Osteogenesis*
Walking
Collagen