Anesth Pain Med.  2019 Jan;14(1):40-43. 10.17085/apm.2019.14.1.40.

Successful intubation using video laryngoscope in a child with CHARGE syndrome: A case report

• Kim J
• Hong JI
• Chae KL
• Yoon KS
• Park SY
• Lee SC
• Lee JH
• Chung CJ
• Choi SR

• KMID: 2434197
• DOI: http://doi.org/10.17085/apm.2019.14.1.40

Abstract

CHARGE syndrome is a rare genetic disorder with CHD7 gene mutation. CHARGE is an acronym for coloboma (C), heart disease (H), atresia of choanae (A), retardation of growth (R), genitourinary malformation (G), and ear abnormalities (E). Patients with CHARGE syndrome need to undergo many surgeries due to their various congenital anomalies. Since airway abnormalities frequently accompany CHARGE syndrome, general anesthesia remains a challenge. Here we report a case of difficult intubation in a 35-month-old boy with CHARGE syndrome during general anesthesia and the experience of successful intubation using D-blade of C-MAC® video laryngoscope.

Keyword

Airway management; CHARGE syndrome; Laryngoscope; Pediatrics

MeSH Terms

Airway Management
Anesthesia, General
CHARGE Syndrome*
Child*
Child, Preschool
Coloboma
Ear
Heart Diseases
Humans
Intubation*
Laryngoscopes*
Male
Nasopharynx
Pediatrics

Figure

• 

  Fig. 1 Arytenoid cartilages and opening of glottis were identified on a monitor of the C-MAC® video laryngoscope.

• 

  Fig. 2 After entering larynx, tube was rotated 180° to enter glottis due to anterior location of larynx and acute angle of video laryngoscope.

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