Ann Clin Neurophysiol.  2019 Jan;21(1):61-65. 10.14253/acn.2019.21.1.61.

Motor dominant polyradiculopathy with Primary Sjögren's syndrome mimicking motor neuron disease

• Ahn SW
• Yoon BN

• KMID: 2434190
• DOI: http://doi.org/10.14253/acn.2019.21.1.61

Abstract

Sjögren's syndrome (SS)-associated polyradiculopathy is rarely reported. A 51-year-old woman presented with a history of gradual weakness in all four extremities for several months. Based on electrophysiological studies, spinal magnetic resonance imaging and cerebrospinal fluid examination, inflammatory polyradiculopathy was confirmed. During a search for the aetiology, the patient was ultimately diagnosed with SS. This study introduces SS-associated polyradiculopathy that primarily presented with motor symptoms, thus mimicking motor neuron disease.

Keyword

Polyradiculopathy; Sjögren's syndrome; Motor neuron disease

MeSH Terms

Cerebrospinal Fluid
Extremities
Female
Humans
Magnetic Resonance Imaging
Middle Aged
Motor Neuron Disease*
Motor Neurons*
Polyradiculopathy*

Figure

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  Fig. 1. Cervical and thoracic spinal MRI. A T2 sagittal image (A) and T1 gadolinium-enhanced sagittal image (B) show unremarkable findings. T1 gadolini-um-enhanced axial images at the (C) C4 level and (D) C6 level show enhancement of the ventral nerve rootletsof the ventral nerve rootlets (white arrows). MRI, magnetic resonance imaging.

Reference

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