Korean J Dermatol.  2019 Jan;57(1):36-39.

A Rare Case of Juvenile Pemphigus Vulgaris Treated with Intravenous Immunoglobulin

Affiliations
  • 1Department of Dermatology, Soonchunhyang University Bucheon Hospital, Bucheon, Korea. shlee@schmc.ac.kr
  • 2Department of Dermatology, Soonchunhyang University Cheonan Hospital, Cheonan, Korea.
  • 3Department of Dermatology, Soonchunhyang University Seoul Hospital, Seoul, Korea.

Abstract

Juvenile pemphigus vulgaris (JPV) is a rare variant of pemphigus vulgaris (PV) occurring in childhood and adolescence that has similar symptoms and the same histological and immunopathological features as classic adult PV. Although rare, advanced cases of JPV can be fatal due to secondary sepsis. Many patients with JPV are misdiagnosed and therefore not properly treated in the early stages of the disease. Although systemic corticosteroids are the therapeutic mainstay, long-term corticosteroid use has various adverse effects. Intravenous immunoglobulin (IVIG) was recently reported to reduce the side effects of corticosteroids. Here, we report a case of JPV in a 14-year-old boy treated with IVIG.

Keyword

Intravenous immunoglobulin; Juvenile pemphigus vulgaris

MeSH Terms

Adolescent
Adrenal Cortex Hormones
Adult
Humans
Immunoglobulins*
Immunoglobulins, Intravenous
Male
Pemphigus*
Sepsis
Adrenal Cortex Hormones
Immunoglobulins
Immunoglobulins, Intravenous
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