J Korean Assoc Pediatr Surg.
1999 Dec;5(2):137-140. 10.13029/jkaps.1999.5.2.137.
Spleen Rupture in Congenital Afibrinogenemia
- Affiliations
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- 1Department of Surgery, Ulsan University College of Medicine, Seoul, Korea.
- KMID: 2422180
- DOI: http://doi.org/10.13029/jkaps.1999.5.2.137
Abstract
- Congenital afibrinogenemia is a rare disorder that refers to a congenital lack of production of fibrinogen, a key component of the hemostatic system. Bleeding manifestations of congenital afibrinogenemia vary in severity from mild to catastrophic. This is a case report of splenic rupture occurred in an eight-year-old boy with congenital afibrinogenemia. Nonoperative treatment with cryoprecipitate and virally inactivated, purified fibrinogen concentrates successfully avoided splenectomy.
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