J Korean Assoc Pediatr Surg.  1999 Dec;5(2):111-115. 10.13029/jkaps.1999.5.2.111.

Hepatic Portojejunostomy for Biliary Atresia

Affiliations
  • 1Division of Pediatric Surgery, Department of Surgery, University of Ulsan College of Medicine and Asan Medical Center, Seoul, Korea.

Abstract

The results of hepatic portojejunostomy in 34 patients with biliary atresia operated upon by one surgeon between May 1989 and December 1997 were analyzed. Eleven (32.3 %) patients were 60 days or younger, 14 patient (41.2 %) were between 60 and 90 days, and 9 (26.5 %) were over 90 days of age. Jaundice cleared in 20 cases (58.8 %). Three patients died of liver insufficiency, 2 were anicteric but died from esophageal variceal bleeding. Three patients died as a result of sepsis, heart failure and left kidney agenesis. Five patients were lost to follow-up. The five-year survival rate was 73.8 %. Two patients over 90 days of age, survived more than 5 years. Survival rates were not significantly related to the age at operation. We conclude that hepatic portojejunostomy should be considered as a primary surgical modality for biliary atresia, even at age 90 days or more. Early detection of esophageal varices and sclerotherapy may be necessary. Liver transplantation is necessary if hepatic failure develops.

Keyword

Biliary atresia; Portoenterostomy

MeSH Terms

Biliary Atresia*
Esophageal and Gastric Varices
Heart Failure
Hepatic Insufficiency
Humans
Jaundice
Kidney
Liver Failure
Liver Transplantation
Lost to Follow-Up
Sclerotherapy
Sepsis
Survival Rate
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