J Korean Soc Radiol.  2018 Jun;78(6):404-407. 10.3348/jksr.2018.78.6.404.

Dynamic Contrast-Enhanced CT Findings of a Extrapleural Solitary Fibrous Tumor in the Spleen: A Case Report and Literature Review

• Kim TK
• Han HY
• Kim JH

• KMID: 2412358
• DOI: http://doi.org/10.3348/jksr.2018.78.6.404

Abstract

Extrapleural solitary fibrous tumor, formerly referred to as "hemangiopericytoma" is a rare soft tissue vascular tumor which has elevated malignancy potential arising from the capillary pericytes. Extrapleural solitary fibrous tumors, originating from the spleen, are extremely rare. We report on a rare case of a patient presenting with splenic extrapleural solitary fibrous tumors with intratumoral irregular calcification detected by dynamic contrast-enhanced computed tomography.

MeSH Terms

Calcinosis
Capillaries
Hemangiopericytoma
Humans
Pericytes
Solitary Fibrous Tumors*
Spleen*
Tomography, X-Ray Computed*

Figure

• 

  Fig. 1 Extrapleural solitary fibrous tumor in spleen of a 35-year-old woman. A. Lobulated margin, irregular shape, dense calcifications with multifocal intratumoral radiolucent areas are displayed on the abdomen erect film. B, C. Coronal (B) and sagittal (C) reformed CT images of extrapleural solitary fibrous tumor show low attenuation foci in large mass (arrow). D. Bizzarre shape calcification is located in central portion (arrowheads) on non-enhanced CT. The mass shows intense enhancement in the central portion (black arrows) and faint in peripheral part of the tumor (white arrows) in the different phases. E. Gross pathologic examination (first image) shows a well circumscribed, nonencapsulated mass, showing extensive hyalinization, dystrophic calcification, and hemorrhage. Hematoxylin and eosin staining shows that the tumor was composed of thin-walled branching hemangiopericytoma-like vessels (second image, arrows), extensive stromal and perivascular hyalinization (third image) and dystrophic calcification in the center of tumor (fourth image, arrows) (× 100). CT = computed tomography

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