Korean J Ophthalmol.  2017 Oct;31(5):462-463. 10.3341/kjo.2017.0042.

Acute Angle Closure Glaucoma in a Patient with Pseudoxanthoma Elasticum

• Han JY
• Lee CE
• Kim YC

• KMID: 2390291
• DOI: http://doi.org/10.3341/kjo.2017.0042

Abstract

No abstract available.

MeSH Terms

Glaucoma, Angle-Closure*
Humans
Pseudoxanthoma Elasticum*

Figure

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  Fig. 1 (A) Photograph of the patient's neck showing multiple, yellowish, f lat papules. (B,C) Biopsy of a skin lesion showing short, curled elastic fibers with basophilic calcification of the reticular dermis which are characteristics of pseudoxanthoma elasticum. Hematoxylin-eosin stain, ×40 original magnification (B), ×200 original magnification (C). (D,E) Fundus photographs (D: right, E: left) showing bilateral angioid streaks, which are narrow and irregular lines emanating from the optic disc. (F,G) Optical coherence tomographic images (F: right, G: left) showing pigment epithelial detachment and breaks in Bruch's membrane at the sites of angioid streaks. (H,I) Photographs during cataract surgery. (H) Iris retractors are placed at the capsulorrhexis edge (arrowheads) to support the area with zonular weakness. (I) A capsular tension ring (arrow) is inserted before intraocular lens implantation to stabilize the capsular bag.

Reference

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