Korean J Thorac Cardiovasc Surg.  2015 Dec;48(6):415-418. 10.5090/kjtcs.2015.48.6.415.

Isolation of the Left Subclavian Artery with Right Aortic Arch in Association with Bilateral Ductus Arteriosus and Ventricular Septal Defect

• Lee JS
• Park JY
• Ko SM
• Seo DM

• KMID: 2382300
• DOI: http://doi.org/10.5090/kjtcs.2015.48.6.415

Abstract

Right aortic arch with isolation of the left subclavian artery is a rare anomaly. The incidence of bilateral ductus arteriosus is sporadic, and a right aortic arch with isolation of the left subclavian artery in association with bilateral ductus arteriosus is therefore extremely rare. Since the symptoms and signs of isolation of the left subclavian artery can include the absence or underdevelopment of the left arm, subclavian steal syndrome, or pulmonary artery steal syndrome, the proper therapeutic approach is controversial. We report a case in which surgical reconstruction was used to treat isolation of the left subclavian artery with right aortic arch in association with bilateral ductus arteriosus and a ventricular septal defect.

Keyword

Aorta, arch; Congenital heart disease; Embryology

MeSH Terms

Aorta, Thoracic*
Arm
Ductus Arteriosus*
Embryology
Heart Defects, Congenital
Heart Septal Defects, Ventricular*
Incidence
Pulmonary Artery
Subclavian Artery*
Subclavian Steal Syndrome