Korean J Thorac Cardiovasc Surg.
2015 Aug;48(4):272-276. 10.5090/kjtcs.2015.48.4.272.
Valve Sparing Aortic Root Replacement in Children with Loeys-Dietz Syndrome
- Affiliations
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- 1Department of Thoracic and Cardiovascular Surgery, Saint Carollo General Hospital, Korea.
- 2Division of Pediatric Cardiac Surgery, Asan Medical Center, University of Ulsan College of Medicine, Korea. pkjj@amc.seoul.kr
- 3Division of Pediatric Cardiology, Asan Medical Center, University of Ulsan College of Medicine, Korea.
- 4Department of Radiology and Research Institute of Radiology, Asan Medical Center, University of Ulsan College of Medicine, Korea.
- KMID: 2382271
- DOI: http://doi.org/10.5090/kjtcs.2015.48.4.272
Abstract
- Loeys-Dietz syndrome (LDS) is an autosomal dominant connective tissue disorder that is characterized by aggressive arterial and aortic disease, often involving the formation of aortic aneurysms. We describe the cases of two children with LDS who were diagnosed with aortic root aneurysms and successfully treated by valve-sparing aortic root replacement (VSRR) with a Valsalva graft. VSRR is a safe and suitable operation for children that avoids prosthetic valve replacement.
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