J Clin Neurol.  2016 Jan;12(1):117-118. 10.3988/jcn.2016.12.1.117.

Early Transneuronal Degeneration in Dyke-Davidoff-Masson Syndrome

• Gupta A
• Goyal MK
• Singh P
• Lal V

• KMID: 2364929
• DOI: http://doi.org/10.3988/jcn.2016.12.1.117

Abstract

No abstract available.

Figure

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  Fig. 1 A and B: T1-weighted axial brain MRI showing (A) diffuse left cerebral hemiatrophy with dilated sulci and left calvarial thickening and (B) hyperaeration of the left frontal sinus. C: T2-weighted (T2W) fluid-attenuated inversion recovery axial brain MRI showing ipsilateral atrophy of the cerebral peduncle (left). D: T2W coronal brain MRI showing crossed cerebellar atrophy (right).

Reference

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2. Carrazana EJ, Liu GT, Holmes GL. Crossed cerebellar atrophy in the Dyke-Davidoff-Masson syndrome. Neuroradiology. 1992; 34:326–327.

3. Cowan WM. Anterograde and Retrograde Transneuronal Degeneration in the Central and Peripheral Nervous System. New York: Springer;1970. p. 217–251.

4. Winkler DT, Probst A, Wegmann W, Tolnay M. Dyke Davidoff Masson syndrome with crossed cerebellar atrophy: an old disease in a new millenium. Neuropathol Appl Neurobiol. 2001; 27:403–405.