Korean J Ophthalmol.  2015 Aug;29(4):282-283. 10.3341/kjo.2015.29.4.282.

A Case of Congenital Simple Hamartoma of the Retinal Pigment Epithelium and Coats' Disease in the Same Eye

• Heo WJ
• Park DH
• Shin JP

• KMID: 2363774
• DOI: http://doi.org/10.3341/kjo.2015.29.4.282

Abstract

No abstract available.

MeSH Terms

Diagnosis, Differential
Fluorescein Angiography
Fundus Oculi
Hamartoma/*congenital/diagnosis
Humans
Male
Retinal Diseases/*congenital/diagnosis
Retinal Pigment Epithelium/*pathology
Retinal Telangiectasis/*diagnosis
Tomography, Optical Coherence
Young Adult

Figure

• 

  Fig. 1 (A) Fundus photograph at initial examination of the right eye shows a small, well-circumscribed, darkly pigmented mass involving the fovea. Telangiectasia of retinal vessels and yellowish-white exudation are also seen in the temporal midperipheral retina. (B) Early phase of fluorescein angiography shows blockage of fluorescence in the fovea due to a mass lesion and a halo of hyperfluorescence around the foveal mass lesion. In the temporal midperipheral retina, aneurysmal dilatation of retinal vessels and hypofluorescence due to exudation and capillary drop-out are seen. (C) Late phase of fluorescein angiography shows subtle leakage around the foveal mass lesion and vascular leakage in the temporal midperipheral retina. (D) Spectral domain optical coherence tomography of the right eye shows a highly reflective, well-defined retinal elevation with complete optical shadowing of the fovea.

Reference

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