Korean J Radiol.  2016 Apr;17(2):302-305. 10.3348/kjr.2016.17.2.302.

A Pulmonary Sequestered Segment with an Aberrant Pulmonary Arterial Supply: A Case of Unique Anomaly

• Kim M
• Woo JJ
• An JK
• Jung YY
• Choi YS

• KMID: 2360218
• DOI: http://doi.org/10.3348/kjr.2016.17.2.302

Abstract

We presented a rare case of a 64-year-old man with a combined anomaly of the bronchus and pulmonary artery that was detected incidentally. Computed tomography showed a hyperlucent, aerated sequestered segment of the right lower lung with an independent ectopic bronchus, which had no connection to the other airway. The affected segment was supplied by its own aberrant pulmonary artery branch from the right pulmonary trunk. This anomaly cannot be classified with any of the previously reported anomalies.

Keyword

Computed tomography; Airway anomaly; Aberrant pulmonary artery

MeSH Terms

Bronchi/pathology
Bronchopulmonary Sequestration/*radiography
Humans
Lung/*radiography
Male
Middle Aged
Pulmonary Artery/*radiography
Tomography, X-Ray Computed

Figure

• 

  Fig. 1 Pulmonary sequestered segment with aberrant pulmonary arterial supply in 64-year-old man. A. 64-year-old man with hyperlucent right lower lobe (arrows). B. Lung window CT at full inspiration shows hyperlucent abnormal lung parenchyma located in lower medial zone of right lower lobe. White arrow (image on left) indicates tortous bronchiectatic bronchus and black arrow (image on right) indicates peripheral bronchiolectasia with bubbly appearance, connected to ectopic bronchus. C. Oblique coronal minimal intensity projection reconstruction shows proximal obliteration of right lower lobe segmental bronchus (arrow) and no visible communication between bronchial tree and ectopic bronchus (arrowhead) in hyperlucent lung. D. Three-dimensional volume rendering image shows anomalous segmental right pulmonary artery (arrows) arising from posteroinferior aspect of right pulomonary trunk. E. HRCT taken in inspiratory (image on left) and expiratory (image on right) phases. There are multiple small cyst-like or emphysematous lesions (in dotted line) in peripheral zone of affected hyperlucent segment. In expiratory phase HRCT, airtrapping in affected area is prominent, in comparison with normal contralateral lung. HRCT = high-resolution CT

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