J Korean Soc Radiol.  2016 Nov;75(5):404-409. 10.3348/jksr.2016.75.5.404.

Magnetic Resonance Imaging Findings of Solitary Infantile Myofibromatosis of the Skull: A Case Report

• Lee SE
• Cho KH
• Suh JH
• Choi JH

• KMID: 2355996
• DOI: http://doi.org/10.3348/jksr.2016.75.5.404

Abstract

Infantile myofibromatosis is a rare, benign mesenchymal disorder of early childhood characterized by solitary or multiple benign myofibroblastic tumors. The tumors may involve the skin, subcutaneous tissue, muscle, bone and visceral organs. We report magnetic resonance imaging findings of solitary infantile myofibromatosis arising in the temporal bone of a ten-month-old boy, and the diagnosis was confirmed by surgical excision and histopathological examination.

MeSH Terms

Diagnosis
Humans
Magnetic Resonance Imaging*
Male
Myofibroblasts
Myofibromatosis*
Skin
Skull*
Subcutaneous Tissue
Temporal Bone

Figure

• 

  Fig. 1 The AP (A) and lateral (B) radiographs of the skull demonstrate a well-defined expansile osteolytic lesion with a thin sclerotic rim in the right temporal bone (arrowheads).

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  Fig. 2 MR images of solitary infantile myofibromatosis of the skull (arrows).

• 

  Fig. 3 Gross findings of the skull mass and whole-mount section.

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  Fig. 4 Microscopic findings.

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