Korean J Spine.
2016 Sep;13(3):170-172. 10.14245/kjs.2016.13.3.170.
Clinical Experiences of Uncommon Motor Neuron Disease: Hirayama Disease
- Affiliations
-
- 1Department of Neurosurgery, Gyeongsang National University Hospital, Gyeongsang National University School of Medicine, Jinju, Korea. ns4793@hanmail.net
- 2Department of Radiology, Gyeongsang National University Hospital, Gyeongsang National University School of Medicine, Jinju, Korea.
- KMID: 2354720
- DOI: http://doi.org/10.14245/kjs.2016.13.3.170
Abstract
- Hirayama disease, juvenile muscular atrophy of the distal upper limb, is a rare disease predominantly affecting the anterior horn cells of the cervical spinal cord in young men. This cervical myelopathy is associated with neck flexion. It should be suspected in young male patients with a chronic history of weakness and atrophy involving the upper extremities followed by clinical stability in few years. Herein, we report 2 cases of Hirayama disease on emphasis of diagnostic approach and describe the pathognomonic findings at flexion magnetic resonance imaging.
