J Clin Neurol.  2016 Apr;12(2):238-240. 10.3988/jcn.2016.12.2.238.

Immunoglobulin G4-Related Hypertrophic Pachymeningitis Mimicking Chiari Malformation

• Kim SH
• Kim JS

• KMID: 2354147
• DOI: http://doi.org/10.3988/jcn.2016.12.2.238

Abstract

No abstract available.

MeSH Terms

Immunoglobulins*
Meningitis*
Immunoglobulins

Figure

• 

  Fig. 1 Serial brain MRI. A: Initial MRI without a contrast agent performed 3 months after symptom onset revealed a cerebellar tonsillar herniation at 5 mm below the foramen magnum, which was consistent with Chiari malformation type I. B: Follow-up MRI performed 5 months later with gadolinium enhancement disclosed hypertrophic pachymeningitis consisting of diffusely thickened dura mater and space-occupying nodular lesions compressing the left pontine tegmentum and right acoustic meatus. C: MRI performed 3 months after steroid treatment revealed marked improvement of the meningeal enlargement and disappearance of the nodular lesions.

Reference

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