J Clin Neurol.  2016 Apr;12(2):238-240. 10.3988/jcn.2016.12.2.238.

Immunoglobulin G4-Related Hypertrophic Pachymeningitis Mimicking Chiari Malformation

Affiliations
  • 1Department of Neurology, Seoul National University College of Medicine, Seoul National University Bundang Hospital, Seongnam, Korea. jisookim@snu.ac.kr

Abstract

No abstract available.


MeSH Terms

Immunoglobulins*
Meningitis*
Immunoglobulins

Figure

  • Fig. 1 Serial brain MRI. A: Initial MRI without a contrast agent performed 3 months after symptom onset revealed a cerebellar tonsillar herniation at 5 mm below the foramen magnum, which was consistent with Chiari malformation type I. B: Follow-up MRI performed 5 months later with gadolinium enhancement disclosed hypertrophic pachymeningitis consisting of diffusely thickened dura mater and space-occupying nodular lesions compressing the left pontine tegmentum and right acoustic meatus. C: MRI performed 3 months after steroid treatment revealed marked improvement of the meningeal enlargement and disappearance of the nodular lesions.


Reference

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