J Pathol Transl Med.  2016 Jul;50(4):312-314. 10.4132/jptm.2015.11.12.

Carney Complex with Multiple Cardiac Myxomas, Pigmented Nodular Adrenocortical Hyperplasia, Epithelioid Blue Nevus, and Multiple Calcified Lesions of the Testis: A Case Report

Affiliations
  • 1Department of Pathology, Gachon University Gil Medical Center, Incheon, Korea.
  • 2Department of Surgery, Gachon University Gil Medical Center, Incheon, Korea.
  • 3Department of Thoracic and Cardiovascular Surgery, Gachon University Gil Medical Center, Incheon, Korea. kkyypak@gilhospital.com

Abstract

No abstract available.


MeSH Terms

Carney Complex*
Hyperplasia*
Myxoma*
Nevus, Blue*
Testis*

Figure

  • Fig. 1. Cardiac myxoma. (A) The gross photo of resected myxoma shows diffusely hyperemic and focally myxoid appearance. (B) Histologically, the tumor is composed of fusiform to stellate cells and surrounding blueish myxoid stroma. Primary pigmented nodular adrenocortical disease. (C) The gross photo of cut surface of resected adrenal glands show round to oval dark brown nodules throughout the cortex. (D) Histologically, the nodules are consisted of large polygonal cells with eosinophilic cytoplasm and granular brown pigments. Epithelioid blue nevus. (E) On low power view, the melanocytic lesion is in dumbbell-shaped and shows prominent dark pigmentation. (F) The tumor cells have relatively abundant eosinophilic cytoplasm and epithelioid appearance. The tumor cells are positive for S-100 protein (G) and human melanoma black 45 (H) immunostains. (I) The testicular biopsy showed large polygonal cells surrounded by hyalinized collagenous stroma and lymphocytic infiltration.


Reference

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