J Korean Ophthalmol Soc.  2013 Aug;54(8):1293-1297.

Retinitis Pigmentosa Complicated by Vitreous Hemorrhage in a Young Patient: A Case Report

• Chung IY
• Huh HD
• Kim SJ
• Han YS
• Seo SW
• Park JM

Abstract

PURPOSE
To report a case of a young male patient with retinitis pigmentosa (RP) accompanied by vitritis and neovascularization of the optic disk in both eyes who underwent unilateral vitrectomy for the treatment of vitreous hemorrhage in the right eye.
CASE SUMMARY
An 8-year-old boy visited our clinic with a complaint of night blindness. Both eyes showed inflammatory cells in the anterior vitreous and neovascularization of the optic disk confirmed by fluorescein angiography. Extensive vitreous hemorrhage developed in his right eye and he underwent unilateral vitrectomy. His final visual acuity was 0.6 in both eyes.
CONCLUSIONS
Vitreous hemorrhage may be related to chronic inflammation in the vitreous and is a very rare RP complication. Vitrectomy can be an effective treatment option for RP complicated by vitreous hemorrhage.

Keyword

Retinitis pigmentosa (RP); Vitrectomy; Vitreous hemorrhage

MeSH Terms

Eye
Fluorescein Angiography
Humans
Inflammation
Male
Night Blindness
Optic Disk
Retinitis
Retinitis Pigmentosa
Visual Acuity
Vitrectomy
Vitreous Hemorrhage

Figure

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  Figure 1. (A, B) Fundus photographs show diffuse retinal degeneration with sparing of the macula in both eyes. (C, D) Electroretinograms showing nearly reduced ‘a’ and ‘b’ waves in the both eyes.

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  Figure 2. (A, B) Fluorescein angiogram of the both eyes show dye leakage from new vessels around the optic disc margin.

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  Figure 3. Fundus photographs show a complete resolusion of the vitreous hemorrhage. (A) Preoperative fundus photograph. (B) Postoperative fundus photograph at 1 month after vitrectomy.

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  Figure 4. Humphrey visual field test. The test shows peripheral field constriction of the both eyes.

Reference

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