J Korean Cleft Palate-Craniofac Assoc.  2000 Oct;1(1):109-114.

Modification of Le Fort III Osteotomy and Fronto-orbital Advancement for the Correction of Crouzon's Disease

• Lee JS
• Lee JG
• Kim CS
• Ha JW

Abstract

In 1912, Crouzon reported one of craniofacial dysostosis, which was inherited as an autosomal dominant trait and characterized by craniosynostosis, midface hypoplasia, and exorbitism. In 1950, the first midface advancement was performed by means of a total facial osteotomy by Sir Harold Gillies. In 1967, Tessier accomplished complete craniofacial dysjunction by performing Le Fort III-Tessier I osteotomy on the basis of Le Fort III fracture and laid the foundation for modern craniofacial surgery. Variable combinations of the surgeries and osteotomies are performed considering functional disabilities as well as patient's age, general condition, and aesthetic problems. The nineteen-year-old female patient complained of frog-like face and showed severe exorbitism and midface hypoplasia, while the occlusion, being relatively normal. We applied modified Le Fort III osteotomy and fronto- orbital advancement. Over the follow-up period of six months, her previous normal occlusion was preserved and the exorbitism and midface deformity largely improved aesthetically.

Keyword

Crouzon's disease; exorbitism; modified Le Fort III osteotomy and fronto-orbital advancement

MeSH Terms

Congenital Abnormalities
Craniofacial Dysostosis*
Craniosynostoses
Female
Follow-Up Studies
Humans
Orbit
Osteotomy*