Obstet Gynecol Sci.  2016 Jul;59(4):342-345. 10.5468/ogs.2016.59.4.342.

A successful laparoscopic neovaginoplasty using peritoneum in Müllerian agenesis with inguinal ovaries accompanied by primary ovarian insufficiency

• Gweon S
• Lee J
• Hwang S
• Hwang KJ
• Kim M

• KMID: 2329060
• DOI: http://doi.org/10.5468/ogs.2016.59.4.342

Abstract

The combination of Müllerian agenesis with inguinal ovaries accompanied by primary ovarian insufficiency is extremely rare. A 21-year-old Korean woman was referred to our center with primary amenorrhea. The patient was diagnosed with Müllerian agenesis with inguinal ovaries. Her hormonal profile showed hypergonadotrophic hypogonadism suggesting primary ovarian insufficiency. We performed laparoscopic neovaginoplasty using modified Davydov's procedure and reposition inguinal ovaries in the pelvic cavity. Oral estrogen replacement was applied for the treatment of primary ovarian insufficiency. This is a rare case report on Mayer-Rokitansky-Kuster-Hauser syndrome accompanied not only by inguinal ovaries but also with primary ovarian insufficiency. We present our first experience on the laparoscopic neovaginoplasty performed on the patient with müllerian agenesis accompanied by inguinal ovaries and primary ovarian insufficiency.

Keyword

Inguinal ovary; Laparoscopy; Müllerian agenesis; Neovaginoplasty; Primary ovarian insufficiency

MeSH Terms

Amenorrhea
Estrogen Replacement Therapy
Female
Humans
Hypogonadism
Laparoscopy
Ovary*
Peritoneum*
Primary Ovarian Insufficiency*
Young Adult

Figure

• 

  Fig. 1 Bilateral inguinal ovaries (arrows). Magnetic resonance imaging (A) and laparoscopic finding (B,C). Vaginal vault (D) was made through middle purstring suture to prevent vaginal prolapse and maintain of vaginal sufficient length after inguinal ovaries reposition.

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  Fig. 2 Postoperative appearance of the newly created vaginal openning (A), 15 days after surgery, the edge of pelvic peritoneum (B), and vaginal vault after surgery at 12 months (C).

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