J Korean Surg Soc.  2005 Jul;69(1):88-91.

Peutz-Jeghers Syndrome with Recurrent Intussusception

• Lee MJ
• Kim JH
• Hwang Y

Abstract

The Peutz-Jeghers syndrome is an autosomal dominant hereditary disease characterized by hamartomatous polyps of the gastrointestinal tract and by mucocutaneous melanin deposits. This syndrome is clinically important because of the complication caused by the gastrointestinal polyp, leading to abdominal pain, gastrointestinal bleeding and intussusception. We experienced a case of Peutz-Jeghers syndrome associated with intussusception who was operated due to intussusception 14 years ago.

Keyword

Peutz-Jeghers syndrome; Intussusception

MeSH Terms

Abdominal Pain
Gastrointestinal Tract
Genetic Diseases, Inborn
Hemorrhage
Intussusception*
Melanins
Peutz-Jeghers Syndrome*
Polyps
Melanins