Tuberc Respir Dis.
1997 Oct;44(5):1184-1193.
A Case of Pulmonary Lymphangioleiomyomatosjs Associated with Thberous Sclerosis and Renal Angiomyolipoma
- Affiliations
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- 1Department of Internal Medical Nowon Eulji Medical Center, Seoul, Korea.
- 2Department of Chest Surgery Nowon Eulji Medical Center, Seoul, Korea.
- 3Department of Uroloy Nowon Eulji Medical Center, Seoul, Korea.
- 4Department of Radiology Nowon Eulji Medical Center, Seoul, Korea.
- 5Department of Anatomical Pathology Nowon Eulji Medical Center, Seoul, Korea.
Abstract
- Lymphangioleiomyomatosis(LAM) is rare and essentially limited to women in the reproductive ages. A 39-year-old female was admitted due to progressive exerUional dyspnea and intermittent productive cough. Chest PA showed marked hyperinflation of the lung associated with a diffuse reticulo-nodular pattern. High resolution CT scan of the thorax demonstrated that diffusely scattered thin-walled cysts were distributed throughout the bilateral lung fields. Abdominal CT scan showed variable sized multiple angiomyolipoma of both kidney. By open lung biopsy, she was diagnosed as pulmonary LAM associated with Tuberous sclerosis and renal Angiomyolipoma. We present the case and discuss the connection between pulmonary LAM and Tuberous sclerosis.
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