Pediatr Allergy Respir Dis.
2009 Dec;19(4):434-439.
A Case of Pulmonary Sequestration and Congenital Lobar Emphysema Presenting with Congestive Heart Failure and Pulmonary Hypertension
- Affiliations
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- 1Department of Pediatrics, Samsung Medical Center Sungkyunkwan University School of Medicine, Seoul, Korea. herz.huh@samsung.com
- 2Department of Thoracic and Cardiovascular Surgery, Samsung Medical Center Sungkyunkwan University School of Medicine, Seoul, Korea.
Abstract
- Congenital cystic disease of the lung represents pulmonary sequestration, congenital lobar emphysema, bronchogenic cyst and congenital cystic adenomatoid malformation. It has a variety of clinical manifestations from immediate postnatal respiratory distress to heart failure. Pulmonary sequestration sometimes causes heart failure in neonates through a shunt between an anomalous systemic feeding artery and the pulmonary venous system. We hereby report a case with both pulmonary sequestration and congenital lobar emphysema presenting with congestive heart failure and pulmonary hypertension, which improved after lobectomy.