Pediatr Allergy Respir Dis.  2009 Dec;19(4):434-439.

A Case of Pulmonary Sequestration and Congenital Lobar Emphysema Presenting with Congestive Heart Failure and Pulmonary Hypertension

Affiliations
  • 1Department of Pediatrics, Samsung Medical Center Sungkyunkwan University School of Medicine, Seoul, Korea. herz.huh@samsung.com
  • 2Department of Thoracic and Cardiovascular Surgery, Samsung Medical Center Sungkyunkwan University School of Medicine, Seoul, Korea.

Abstract

Congenital cystic disease of the lung represents pulmonary sequestration, congenital lobar emphysema, bronchogenic cyst and congenital cystic adenomatoid malformation. It has a variety of clinical manifestations from immediate postnatal respiratory distress to heart failure. Pulmonary sequestration sometimes causes heart failure in neonates through a shunt between an anomalous systemic feeding artery and the pulmonary venous system. We hereby report a case with both pulmonary sequestration and congenital lobar emphysema presenting with congestive heart failure and pulmonary hypertension, which improved after lobectomy.

Keyword

Pulmonary sequestration; Emphysema; Pulmonary hypertension; Heart failure

MeSH Terms

Arteries
Bronchogenic Cyst
Bronchopulmonary Sequestration
Cystic Adenomatoid Malformation of Lung, Congenital
Emphysema
Estrogens, Conjugated (USP)
Heart Failure
Humans
Hypertension, Pulmonary
Infant, Newborn
Lung
Pulmonary Emphysema
Estrogens, Conjugated (USP)
Pulmonary Emphysema
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