J Korean Pediatr Cardiol Soc.  2006 Sep;10(3):239-252.

Pulmonary Arterial Hypertension with Congenital Heart Diseases

• Lee JH

Abstract

Pulmonary arterial hypertension is a significant complication of congenital heart disease, which carries a recognized risk of morbidity and mortality. There have been remarkable advances in the field of pulmonary arterial hypertension over the past several decades. At the third world symposium on pulmonary arterial hypertension held in Venice, Italy, 2003, congenital cardiac shunts were classified in the same group as idiopathic pulmonary hypertension. This article discusses the recent advances in understanding the pathology, pathobiology, diagnosis, and treatment of pulmonary arterial hypertension associated pediatric congenital heart disease.

Keyword

Pulmonary arterial hypertension; Congenital heart disease; Pediatrics

MeSH Terms

Diagnosis
Heart Defects, Congenital
Heart Diseases*
Heart*
Hypertension*
Hypertension, Pulmonary
Italy
Mortality
Pathology
Pediatrics