Korean J Urol.  2008 Jun;49(6):562-565.

Nephrogenic Diabetes Insipidus Associated with Nonobstructive Dilation of the Urinary Tract and Voiding Difficulty

• Lee JW
• Choi H
• Oh SJ

Abstract

Nephrogenic diabetes insipidus(DI) is characterized by insensitivity of the distal nephron to vasopressin(ADH) and the inability to concentrate urine, which leads to excreting excessive quantities of urine. Upper tract dilation secondary to polyuria was previously shown to be associated with nephrogenic DI. We report here on 3 males with nephrogenic DI that caused voiding difficulty as well as massive nonobstructive dilation of the urinary tract.

Keyword

Diabetes insipidus; Voiding difficulty

MeSH Terms

Diabetes Insipidus
Diabetes Insipidus, Nephrogenic
Humans
Male
Nephrons
Polyuria
Urinary Tract

Figure

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  Fig. 1. Voiding cystourethrogram (A). The “christmas tree” appearance of the bladder was seen on ultrasonography (B). Severe hydronephrosis with dilation of the bladder and diatal ureter was seen.

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  Fig. 2. (A) The uroflowmetry study revealed that the patient was voiding by abdominal straining. (B) The filling cystometrogram (CMG) shows a large bladder capacity with decreased sensation. (C) The voiding CMG demonstrates slightly weak detrusor contractility with abdominal straining.

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