Korean J Dermatol.
2007 Feb;45(2):206-208.
A Case of Fibrosarcomatous Dermatofibrosarcoma Protuberans
- Affiliations
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- 1Department of Dermatology, College of Medicine, Hallym University, Anyang, Korea. kkj51818@hallym.or.kr
Abstract
- Dermatofibrosarcoma protuberans (DFSP) is characterized clinically by a locally aggressive growth and a high rate of local recurrence, but distant metastases and tumor related deaths are very rare. Several histologic variants have been described. Among them, sarcomatous change in DFSP represents a form of tumor progression and is associated with a worse prognosis than ordinary DFSP. As a result, it needs more intense treatment and close follow-up care after treatment. A 50-year-old woman presented with a 6 month history of a solitary, walnut-sized, erythematous, hard fixed nodule on her right lower abdomen. Histopathologic examination revealed increased cytologic atypia and mitotic activity with a herringbone growth pattern and negativity for CD34. We report a case of fibrosarcomatous dermatofibrosarcoma protuberans treated by wide surgical excision.