Korean J Anesthesiol.  2004 Oct;47(4):590-592. 10.4097/kjae.2004.47.4.590.

Anesthetic Management of a Patient with a Single Ventricle and Pheochromocytoma: A case report

• Kim YH
• Oh AY
• Kim CS

• KMID: 2299300
• DOI: http://doi.org/10.4097/kjae.2004.47.4.590

Abstract

Single ventricle is a rare congenital anomaly that accounts for about 1.5% of all congenital heart defects at birth. It is believed to carry a poor prognosis when untreated, which has led to a more aggressive surgical approach in childhood. The surgical approach is an initial palliative operation in the form of a shunt, followed by a Fontan operation or one of its modifications. However, a few case reports have noted the survival of patients to the fifth or sixth decade without surgical repair. We experienced an anesthesia of a 20-year-old female patient for excision of the pheochromocytoma who had chronic hypoxia due to partially corrected single ventricle anomaly. We report this experience with brief review of literature.

Keyword

anesthesia; pheochromocytoma; single ventricle; surgery

MeSH Terms

Anesthesia
Anoxia
Female
Fontan Procedure
Heart Defects, Congenital
Humans
Parturition
Pheochromocytoma*
Prognosis
Young Adult