Korean J Anesthesiol.  2003 Mar;44(3):414-417. 10.4097/kjae.2003.44.3.414.

Anesthetic Management of Myotonic Dystrophy: A case report

Affiliations
  • 1Department of Anesthesiology, College of Medicine, University of Pochon CHA, Sungnam, Korea. lbhaak@hanmail.net

Abstract

Myotonic dystrophy is a muscle disorder characterized by progressive muscle wasting and weakness associated with myotonia. It is a systemic disease transmitted in an autosomal dominant pattern. Myotonia may be precipitated by hypothermia, shivering, and mechanical or electrical stimulation. Furthermore, sensitivity to sedative, anesthetic and neuromusclular blocking agents may result in intraoperative and early postoperative cardiovascular and respiratory complications, as well as prolonged recovery from anesthesia. Therefore, a patient with myotonic dystrophy is at high risk for complications from anesthetic management. We report the successful anesthetic management of such a patient undergoing a total abdominal hysterectomy, in which we used an epidural technique for intraoperative anesthesia and postoperative analgesia.

Keyword

Anesthetic management; myotonic dystrophy

MeSH Terms

Analgesia
Anesthesia
Electric Stimulation
Humans
Hypothermia
Hysterectomy
Muscular Diseases
Myotonia
Myotonic Dystrophy*
Shivering
Full Text Links
  • KJAE
Actions
Cited
CITED
export Copy
Close
Share
  • Twitter
  • Facebook
Similar articles
Copyright © 2024 by Korean Association of Medical Journal Editors. All rights reserved.     E-mail: koreamed@kamje.or.kr