Korean J Spine.  2014 Mar;11(1):15-17. 10.14245/kjs.2014.11.1.15.

Crowned Dens Syndrome: A Case Report and Review of the Literature

• Lee GS
• Kim RS
• Park HK
• Chang JC

• KMID: 2288383
• DOI: http://doi.org/10.14245/kjs.2014.11.1.15

Abstract

The crowned dens syndrome (CDS), also known as periodontoid calcium pyrophosphate dehydrate crystal deposition disease, is typified clinically by severe cervical pain, neck stiffness and atlantoaxial synovial calcification which could be misdiagnosed as meningitis, epidural abscess, polymyalgia rheumatica, giant cell arthritis, rheumatoid arthritis, cervical spondylitis or metastatic spinal tumor. Crystalline deposition on cervical vertebrae is less well known disease entity and only a limited number of cases have been reported to date. Authors report a case of CDS and describe the clinical feature.

Keyword

Neck pain; Calcium pyrophosphate; Axis; Computed tomography

MeSH Terms

Arthritis
Arthritis, Rheumatoid
Axis, Cervical Vertebra
Calcium Pyrophosphate
Cervical Vertebrae
Crowns*
Crystallins
Epidural Abscess
Female
Giant Cells
Meningitis
Neck
Neck Pain
Polymyalgia Rheumatica
Spondylitis
Calcium Pyrophosphate
Crystallins