Korean J Pediatr.  2013 Dec;56(12):545-549. 10.3345/kjp.2013.56.12.545.

Moyamoya syndrome occurred in a girl with an inactive systemic lupus erythematosus

• Lee YJ
• Yeon GM
• Nam SO
• Kim SY

• KMID: 2284793
• DOI: http://doi.org/10.3345/kjp.2013.56.12.545

Abstract

We report the case of a 17-year-old Korean girl with systemic lupus erythematosus (SLE) who presented with sudden weakness of the right-sided extremities and dysarthria. Oral prednisolone was being taken to control SLE. Results of clinical and laboratory examinations did not show any evidence of antiphospholipid syndrome or thromboembolic disease nor SLE activity. Cerebral angiography showed stenosis of the left internal carotid artery and right anterior cerebral artery with accompanying collateral circulation (moyamoya vessels). After the patient underwent bypass surgery on the left side, she recovered from the neurological problems and did not experience any additional ischemic attack during the 14-month follow-up period. This case represents an unusual association between moyamoya syndrome and inactive SLE (inactive for a relatively long interval of 2 years) in a young girl.

Keyword

Moyamoya disease; Systemic lupus erythematosus; Child

MeSH Terms

Adolescent
Anterior Cerebral Artery
Antiphospholipid Syndrome
Carotid Artery, Internal
Cerebral Angiography
Child
Collateral Circulation
Constriction, Pathologic
Dysarthria
Extremities
Female*
Follow-Up Studies
Humans
Lupus Erythematosus, Systemic*
Moyamoya Disease*
Prednisolone
Prednisolone