Korean J Pediatr.  2006 Jun;49(6):696-699. 10.3345/kjp.2006.49.6.696.

A case of Tolosa-Hunt syndrome

• Kim DG
• Kim YO
• Woo YJ

• KMID: 2279896
• DOI: http://doi.org/10.3345/kjp.2006.49.6.696

Abstract

Tolosa-Hunt syndrome is a rare disease in children characterized by dull, persistent pain around the affected eye and ophthalmoplegia caused by granulomatous inflammation in the cavernous sinus, superior orbital fissure, or orbit. Although spontaneous remission can occur, corticosteroids frequently have a dramatic response; however, recurrence can transpire after complete remission. We report an 11-year-old girl with Tolosa-Hunt syndrome who responded to corticosteroid promptly, without complications, but suffered three recurrences of headache and retro-orbital pain and required maintenance on a low dose of steroid.

Keyword

Tolosa-Hunt syndrome; Painful ophthalmoplegia; Headache

MeSH Terms

Adrenal Cortex Hormones
Cavernous Sinus
Child
Female
Headache
Humans
Inflammation
Ophthalmoplegia
Orbit
Rare Diseases
Recurrence
Remission, Spontaneous
Tolosa-Hunt Syndrome*
Adrenal Cortex Hormones