Korean J Pediatr Hematol Oncol.  2005 Apr;12(1):120-124.

A Case of Congenital Hepatoblastoma

Affiliations
  • 1Department of Pediatrics, Pusan National University, College of Medicine, Busan, Korea. limyt@pusan.ac.kr
  • 2Department of Surgery, Pusan National University, College of Medicine, Busan, Korea.

Abstract

Hepatoblastoma is the most common primary malignant hepatic tumor in infancy and childhood. But congenital hepatoblastomas are extremely rare and show distinctive, but important features when compared with tumors diagnosed in children beyond the neonatal age. They have different clinical presentations, higher incidence of pure fetal histology, significant risk for systemic metastasis, and worse outcome. The treatment of congenital hepatoblastoma should be the same as in older children, i.e., primary chemotherapy with delayed resection. We report a case of congenital hepatoblastoma in a 29-day-old boy who was known to have a well-defined ovoid hypoechoic mass at liver demonstrated by fetal sonography.

Keyword

Congenital hepatoblastoma; Worse prognosis

MeSH Terms

Child
Drug Therapy
Hepatoblastoma*
Humans
Incidence
Liver
Male
Neoplasm Metastasis
Full Text Links
  • KJPHO
Actions
Cited
CITED
export Copy
Close
Share
  • Twitter
  • Facebook
Similar articles
    DB Error: unknown error