Korean J Otolaryngol-Head Neck Surg.
2006 Apr;49(4):464-467.
Hereditary Angioneurotic Edema of the Larynx: A Case Report and Literature Review
- Affiliations
-
- 1Department of Otorhinolaryngology-Head and Neck Surgery, College of Medicine, Konkuk University, Seoul, Korea. entalk@kuh.ac.kr
Abstract
-
Hereditary angioneurotic edema (HAE) is an autosomal dominant disease that results from the deficiency of C1 esterase inhibitor (C1-INH) function. Urgent proper intervention of the upper airway is warranted to save the life of patients with the disease, which often causes acute airway obstruction. We present, with a review of literature, a case of 37-year old woman with HAE of larynx.